Haemangioma with thrombocytopenia (Kasabach-Merritt syndrome).
نویسندگان
چکیده
We describe two patients with haemangioma with thrombocytopenia (Kasabach-Merritt syndrome). Both were treated with corticosteroids without notable improvement. The first patient responded satisfactorily to radiotherapy, whereas the second showed a slow spontaneous resolution.
منابع مشابه
Haemangioma, thrombocytopenia and coagulopathy- kasabach merritt syndrome: an appraisal for anaesthesiologists.
Haemangioma is a common type of vascular tumour in paediatric age group [1]. Most of them are benign and non-life threatening [1]. Kasabach Merritt syndrome (KMS) is a combination of giant haemangioma, thrombocytopenia and consumptive coagulopathy [1-5]. It presents with diverse clinical presentation and may be a part of other recognized syndrome [1,2]. KMS is a well-recognized but rare clinica...
متن کاملSplenic haemangioma and Kasabach-Merritt Syndrome as differential diagnosis for abdominal mass in a newborn: case report
Pós-graduando da Seção de Cirurgia Pediátrica. Instituto Nacional de Câncer, Hospital do Câncer I, Rio de Janeiro, RJ Brasil. Médico Cirurgião Pediátrico da Seção de Cirurgia Pediátrica. Instituto Nacional de Câncer, Hospital do Câncer I, Rio de Janeiro, RJ Brasil. Médico Patologista da Seção de Anatomopatologia. Instituto Nacional de Câncer, Hospital do Câncer I, Rio de Janeiro, RJ Brasil. Méd...
متن کاملSuccessful treatment of kasabach-merritt syndrome with vincristine and surgery: a case report and review of literature
INTRODUCTION Haemangiomas are vascular lesions resulting from abnormal proliferation of blood vessels. They are the most common pediatric neoplasm. Kasabach-Merritt syndrome is a rare type of vascular lesion with peculiar characteristics. The diagnosis is based upon three basic findings; enlarging haemangioma, thrombocytopenia and consumption coagulopathy. CASE PRESENTATION A 5 month old boy ...
متن کاملTreatment of a Giant Haemangioma of the Liver With Kasabach-Merritt Syndrome by Orthotopic Liver Transplant
We describe a case of giant cavernous haemangioma of the liver with disseminated intravascular coagulopathy (Kasabach-Merritt syndrome) which was cured by orthotopic liver transplant. A 47 year old man presented with bleeding and tender massive hepatomegaly after tooth extraction. Investigations showed disseminated intravascular coagulopathy and a giant hepatic haemangioma involving both lobes ...
متن کامل[A case report of Kasabach-Merritt syndrome].
Kasabach Merritt syndrome (KMS) is an uncommon complication of large haemangioma in which there is thrombocytopenia and coagulopathy. We report a case of a new born male baby presented with a large haemangioma on the right upper extremity and his initial laboratory tests were consistent with consumptive coagulopathy. He was diagnosed as a case of KMS and treated with oral prednisolone. 1. Assoc...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 58 12 شماره
صفحات -
تاریخ انتشار 1983